Collagen type III glomerulopathy
Synonyms: Collagenofibrotic glomerulopathy
A rare non-immune-mediated glomerular disease characterized by abnormal accumulation of type III collagen within the mesangium and subendothelial space of the glomerulus. Clinically it usually manifests with proteinuria (often in the nephrotic range) microscopic hematuria peripheral edema and/or hypertension. Progression to end-stage kidney failure is possible.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Collagen type III glomerulopathy?
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