Thank you for visiting the RARE List. We recognize how critical accurate information is, and our team is working diligently to bring you a new, complete and accurate RARE List in the coming months. We apologize for this inconvenience. Should you need anything in the meantime, please contact the RARE Concierge Patient Services team.

Adenoid cystic carcinoma of the cervix uteri

Overview

A rare highly aggressive uterine cancer macroscopically appearing as an irregular slow-growing non-friable polypoid mass on the uterine cervix and histologically showing a pseudoglandular or cribriform growth pattern. It presents with vaginal bleeding and discharge and abdominal or pelvic pain. The tumor is highly infiltrative often associated with vascular lymphatic and perineural invasion with subsequent haematogenous spread and early recurrence.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2022.

Connect. Empower. Inspire.