Hypocomplementemic urticarial vasculitis

Get in touch with RARE Concierge.

Contact RARE Concierge

Hypocomplementemic urticarial vasculitis

Synonyms: Anti-C1q vasculitis | Mac Duffie hypocomplementemic urticarial vasculitis | Mac Duffie syndrome | McDuffie hypocomplementemic urticarial vasculitis | McDuffie syndrome

A rare immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C3 C4 and/or C1q) and usually associated with circulating anti-C1q autoantibodies. Arthritis pulmonary disease ocular inflammation are common systemic manifestations.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024

Newly diagnosed with
Hypocomplementemic urticarial vasculitis?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

Clinical Trials

For a list of clinical trials in this disease area, please click here.