Idiopathic recurrent pericarditis
Synonyms: Idiopathic relapsing pericarditis
Idiopathic recurrent pericarditis is a rare autoinflammatory syndrome defined as recurrence of pericardial inflammation of unknown origin following the first episode of acute pericarditis and a symptom-free interval of 4-6 weeks or longer. Recurrent attacks of chest pain may be the sole presentation or the chest pain may be accompanied by pericardial friction rub electrocardiographic or echocardiographic changes pericardial effusion and increased C-reactive protein. Cardiac tamponade is a rare life-threatening complication.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Idiopathic recurrent pericarditis?
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Advocacy Organizations
Autoinflammatory Alliance
https://autoinflammatory.org
Clinical Trials
For a list of clinical trials in this disease area, please click here.