Ocular cicatricial pemphigoid
A rare inflammatory eye disease characterized by sub-epithelial blistering manifesting with bilateral asymmetrical chronic or recurrent conjunctivitis and aberrant tissue regeneration leading to progressive conjunctival fibrosis secondary corneal vascularization and in some cases blindness. Patients typically present with conjunctival redness increased lacrimation burning and/or foreign body sensation edema limbitis and/or varying degrees of ocular pain. Ankyloblepharon may be observed in end stages of the disease.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Ocular cicatricial pemphigoid?
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Advocacy Organizations
International Pemphigus & Pemphigoid Foundation
The mission of the International Pemphigus & Pemphigoid Foundation (IPPF) is to improve the quality of life for all people affected by pemphigus and pemphigoid through early diagnosis and support. Our vision is to find a cure for pemphigus and pemphigoid.
Clinical Trials
For a list of clinical trials in this disease area, please click here.