Pulmonary artery, isolated unilateral absence of (Isolated UAPA)


Type of disease: Rare conditions

An isolated unilateral absence of the pulmonary artery (IUAPA) is the absence of the left or right pulmonary artery. It is a rare condition with an estimated prevalence of less than 1 in 200,000 young adults. Reported symptoms are breathing difficulty, chest pain, coughing up of blood and repeated infections. Diagnosis can be difficult due to the rarity of the condition. IUAPA is usually associated with heart anomalies and surgically treated in childhood.

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