Pulmonary artery, unilateral absence of (UAPA)
Type of disease: Rare conditions
Unilateral absence of pulmonary artery (UAPA) is an isolated unilateral absence of pulmonary artery (IUAPA) in combination with other heart abnormalities. It is a rare condition with an estimated prevalence of 1 in 200,000 young adults. Reported symptoms are breathing difficulty, chest pain, coughing up of blood and repeated infections. Diagnosis can be difficult due to the rarity of the condition. UAPA is usually associated with heart anomalies and surgically treated in childhood.