Acrokeratoelastoidosis of Costa

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Synonyms: AKE | PPKP3 | Punctate palmoplantar hyperkeratosis type 3 | Punctate palmoplantar keratoderma type 3

A rare punctate palmoplantar keratoderma characterized by multiple small round to oval or rhomboid yellowish hyperkeratotic papules and plaques most commonly localized to the palms of the hands and soles of the feet potentially extending to the dorsum of the hands and feet in severe cases. Histopathological analysis shows hyperkeratosis epidermal hypertrophy and fragmentation and rarefaction of elastic fibers. The condition can be sporadic or familial.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version July 2024

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Acrokeratoelastoidosis of Costa?

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