Synonyms: Familial polymorphous light eruption of American Indians | Hereditary polymorphous light eruption of American Indians | Hutchinson summer prurigo | Hydroa aestivale
A rare chronic photodermatosis disease characterized by intensely pruritic polymorphic erythematous excoriated and/or lichenified papules macules plaques and nodules occurring on sun-exposed areas of the skin (particularly face nose lips and ears) frequently associating cheilitis (especially of the lower lip) and conjuctivitis which are present year-round or only in the spring/summer (depending on geographic location) observed mainly in Native Americans and Mestizos. Cheilitis may be the sole clinical presentation. Histologically the presence of lymphoid follicles in mucosa is pathognomonic.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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