Anomalous aortic origin of the right coronary artery

Get in touch with RARE Concierge.

Contact RARE Concierge

Anomalous aortic origin of the right coronary artery

Synonyms: AORCA | R-ACAOS | Right coronary artery from left aortic sinus

A rare coronary artery congenital malformation characterized by an anomalous origin and course of the right coronary artery which originates from the left aortic sinus of Valsalva and has an abnormal proximal course which may be intramural prepulmonic subpulmonic retroaortic retrocardiac or wrapped around the apex. Patients are frequently asymptomatic although chest pain dyspnea palpitations dizziness syncope and sudden cardiac arrest/death (typically following intense physical exertion) may be observed. This malformation is associated with a lower risk of sudden cardiac death therefore surgical revascularization is recommended only when signs and/or symptoms of ischemia are present.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

Newly diagnosed with
Anomalous aortic origin of the right coronary artery?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Clinical Trials

For a list of clinical trials in this disease area, please click here.