Arterial dissection-lentiginosis syndrome
A rare association syndrome reported in several members of two families to date characterized by arterial dissection occurring at an early age and presenting with a range of manifestations depending on the vascular territory involved (ex. headache dysphasia hemiparesis) in association with cystic medial necrosis and multiple lentigines (brown and black in color and mainly affecting the skin of the trunk and extremities).
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Arterial dissection-lentiginosis syndrome?
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