Atypical lichen myxedematosus

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Atypical lichen myxedematosus

Synonyms: Intermediate lichen myxedematosus

An intermediate form of lichen myxedematosus (LM) (a form of mucin dermal deposit) which does not meet the criteria for either scleromyxedema or the localized form. Three clinical subtypes have been described and include scleromyxedema without monoclonal gammopathy; localized forms with monoclonal gammopathy and/or systemic symptoms; localized forms with mixed features of the 5 subtypes of localized LM (discrete form acral persistent papular mucinosis self-healing papular mucinosis papular mucinosis of infancy and a pure nodular form). The course of atypical LM is unpredictable because only a few cases have been reported.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version April 2024

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