Becker nevus syndrome
Synonyms: Pigmentary hairy epidermal nevus
A rare syndromic benign epidermal nevus syndrome characterized by the association of a Becker nevus (i.e. circumscribed unilateral irregularly shaped hyperpigmented macules with or without hypertrichosis and/or acneiform lesions occuring predominantly on the anterior upper trunk or scapular region) with ipsilateral breast hypoplasia or other typically hypoplastic skeletal cutaneous and/or muscular defects such as pectoralis major hypoplasia supernumerary nipples vertebral defects scoliosis limb asymmetry odontomaxillary hypoplasia and lipoatrophy.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Becker nevus syndrome?
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