Carcinoma of the ampulla of Vater

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Carcinoma of the ampulla of Vater

Synonyms: Ampullary carcinoma | Ampulloma

Carcinoma of the ampulla of Vater is a rare malignant tumor originating from the ampulla of Vater that can present with symptoms of general fatigue loss of appetite weight loss nausea vomiting abdominal pain and most commonly painless obstructive jaundice. The tumor is believed to arise from duodenal biliary or pancreatic epilthelium resulting in the respective histological types. In general carcinoma of the ampulla of Vater has a better prognosis (5-year survival rate of 45%) than cancers of the distal bile duct and pancreas.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

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