Clear cell sarcoma of kidney

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Clear cell sarcoma of kidney

Synonyms: CCSK

Clear cell sarcoma of kidney is a rare primary genetic renal tumor usually characterized by a unilateral unicentric morphologically diverse tumor that arises from the renal medulla and has a tendency for vascular invasion. Clinically it presents with a palpable abdominal mass abdominal or flank pain hematuria anemia and/or fatigue. Metastatic spread to lymph nodes bones lungs retroperitoneum brain and liver is common at time of diagnosis and therefore bone pain cough or neurological compromise may be associated. Metastasis to unusual sites such as the scalp neck nasopharynx axilla orbits and epidural space have been reported.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

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Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


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