Cochlear nerve deficiency

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A rare otorhinolaryngological malformation characterized by a hypoplastic or absent cochlear nerve resulting in variable hearing loss or total deafness depending on the quantity of nerve fibers present. The condition can be unilateral or bilateral occur as an isolated malformation or in the context of a complex syndrome and may be associated with a hypoplastic internal auditory or cochlear nerve canal.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. Ā© INSERM 1999. Available on Data version June 2024

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Cochlear nerve deficiency?

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Clinical Trials

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