Complete atrioventricular septal defect

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Complete atrioventricular septal defect

Synonyms: CAVC | Complete AVSD | Complete atrioventricular canal | Complete atrioventricular canal defect | Complete atrioventricular septal defect with atrial and ventricular components

A rare congenital cardiac anomaly characterized by a common atrioventricular junction with a common AV valve an interatrial communication just above the common AV valve (ostium primum defect) a posterior interventricular communication (inlet VSD) that results in shunting at both the atrial and ventricular level. Morphologically the common atrioventricular valve has 4 or 5 leaflets including superior and inferior bridging leaflets with a single annulus.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version April 2024

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Complete atrioventricular septal defect?

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Advocacy Organizations

Genetic Support Network of Victoria

The Genetic Support Network of Victoria is an organisation that supports people living with genetic, undiagnosed and rare conditions and those who support them including community and families, patient support organisations, health professionals and industry. Our vision is our community flourishing and living their best lives.

Clinical Trials

For a list of clinical trials in this disease area, please click here.