Composite hemangioendothelioma

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Composite hemangioendothelioma

A rare vascular tumor characterized by a poorly circumscribed infiltrative nodular lesion with vascular differentiation centered in the dermis and subcutis. The tumor is composed of histologically benign intermediate and malignant components. Typical is an admixture of different components which include epithelioid and retiform hemangioendothelioma spindle cell hemangioma angiosarcoma-like areas and benign vascular lesions. Predilection sites are the distal extremities. Many patients have a history of lymphedema. Local recurrence is frequent while metastasis is rare.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024

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