Congenital aortopulmonary window
Synonyms: Congenital aortopulmonary artery fistula | Congenital aortopulmonary septal defect
A rare congenital non-syndromic heart malformation characterized by a communication between the ascending aorta and the pulmonary trunk in the presence of two normally formed semilunar valves. It may be an isolated finding or occur in association with other anomalies. Severe clinical manifestations such as congestive heart failure or pulmonary hypertension typically develop in early life.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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Congenital aortopulmonary window?
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Clinical Trials
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