Congenital complete agenesis of pericardium is a rare mostly asymptomatic congenital heart malformation characterized by the complete absence of the entire pericardium or by the absence of either the right (uncommon) or left pericardium. It is occasionally associated with chest pain (common) dyspnea dizziness bradycardia and syncope while exertional manifestations are rare. The disease is usually incidentally diagnosed during surgery or at autopsy.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version October 2024
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Congenital complete agenesis of pericardium?
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