Congenital ichthyosiform erythroderma

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Congenital ichthyosiform erythroderma

Synonyms: CIE | Erythrodermic ichthyosis | Non-bullous congenital ichthyosiform erythroderma

A rare autosomal recessive congenital ichthyosis (ARCI) characterized by generalised scaling accompanied by a more or less severe erythroderma without blister formation.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024

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Congenital ichthyosiform erythroderma?

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Clinical Trials

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