Congenital pulmonary airway malformation
Synonyms: CCAM | CPAM | Congenital cystic adenomatoid malformation of the lung | Congenital cystic adenomatous malformation of the lung | Congenital cystic disease of the lung
A rare respiratory malformation characterized by a hamartomatous mass of non-functioning lung tissue of variable extent and with variable degrees of cystic or adenomatoid change. Clinical presentation prognosis and presence of associated abnormalities depend on the subtype of the lesion. Based on histopathological findings five subtypes (types 0 to 4) can be differentiated.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Congenital pulmonary airway malformation?
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