Congenital stenosis of the inferior vena cava

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Congenital stenosis of the inferior vena cava

Synonyms: Congenital stenosis of the IVC | Congenital stenosis of the inferior caval vein

A rare vascular anomaly characterized by congenital narrowing of the inferior vena cava mostly at the diaphragmatic level or hepatic segment with or without web formation. Patients may present with deep vein thrombosis below the obstructed segment as well as swelling pain and varices of the lower extremities abdominal pain/varices or hematochezia. Presence of collateral veins between upper and lower segments of the stenosis as well as venous aneurysms are typical associated findings.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024

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