Congenital systemic arteriovenous fistula

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Congenital systemic arteriovenous fistula is a rare potentially life-threatening vascular malformation characterized by a direct communication between an artery and a vein without the interposition of the capillary bed ocurring in the systemic circulation (mainly the cranium liver lungs extremities and vessels in or near the thoracic wall). Manifestations are variable depending on size and extent of the fistula the involved blood vessels and the precise location of the collaterals and may include systolic or continuous murmur over the affected organ tachycardia increased stroke volume cardiomegaly and increased pulmonary vascular markings.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Congenital systemic arteriovenous fistula?

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