Cor triatriatum sinister
Synonyms: Cor triatriatum sinistrum | Divided left atrium
A rare congenital non-syndromic heart malformation characterized by the presence of a thin fibromuscular membrane subdividing the left atrium into an upper and lower chamber. The upper chamber receives blood from the pulmonary veins and the lower chamber is attached to the left atrial appendage. Therefore the membrane blocks the orifice of the mitral valve and leads to obstruction of the left ventricular inflow. It may be asymptomatic or present in infancy with tachypnea dyspnea hemoptysis chest pain syncope pulmonary edema pulmonary hypertension or heart failure depending on the degree of obstruction. The anomaly may be isolated or associated with other congenital heart anomalies.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Cor triatriatum sinister?
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