Dermatitis herpetiformis
Synonyms: Duhring-Brocq disease
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules urticarial plaques erythema and herpetiform vesiculae with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%) knees (30%) shoulders buttocks sacral region and face of children and adults. Erosions excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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