Synonyms: DCM | Diffuse cutaneous maculopapulous mastocytosis
Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM; see this term) characterized by generalized erythroderma various degrees of blistering skin with a ”peau d’orange” appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized one with extreme blistering (Bullous DCM; see this term) and one with infiltrations (Pseudoxanthomatous DCM; see this term).
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version September 2024
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Diffuse cutaneous mastocytosis?
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