Dysembryoplastic neuroepithelial tumor
Synonyms: DNET
A rare mixed neuronal-glial tumor characterized by a benign usually supratentorial lesion with predominantly cortical location and multinodular architecture. The tumor typically becomes symptomatic in the second or third decade of life with drug-resistant partial seizures. Histological hallmark is the specific glioneuronal element columns oriented perpendicularly to the cortical surface formed by bundles of axons attached to oligodendroglia-like cells while neurons appear to float in an abundant eosinophilic matrix.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Dysembryoplastic neuroepithelial tumor?
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