Elastofibroma dorsi is a rare acquired dermis elastic tissue disorder characterized by a benign slowly progressive often bilateral non-encapsulated lesion usually presenting as an ill-defined mass under the inferior angle of the scapula (but other locations have been reported) which adheres to the deep layers and presents no local signs of inflammation. It is commonly asymptomatic and discovered inadvertently but symptoms may include pain and discomfort or stiffness when using the shoulder. The presence of a firm mass masked by the scapula during retropulsion of the shoulder and becoming prominent when the shoulder is displaced toward the front is a frequent sign. Neuromuscular involvement of the upper limb may occur in rare cases.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version December 2023
Newly diagnosed with
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