Erythrokeratoderma ”en cocardes”
Synonyms: Degos genodermatosis "en cocardes"
A rare genetic epidermal disorder characterized by intermittent (remitting and recurring) annular polycyclic target-like (or ‘en cocardes’) plaques with concentric rings of scaling erythema occurring on the extremities flexural areas and trunk. Concurrent erythrokeratoderma variabilis-like scaly plaques are commonly found in other parts of the body.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Erythrokeratoderma ”en cocardes”?
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