Erythrokeratoderma ”en cocardes”
Synonyms: Degos genodermatosis "en cocardes"
A rare genetic epidermal disorder characterized by intermittent (remitting and recurring) annular polycyclic target-like (or ‘en cocardes’) plaques with concentric rings of scaling erythema occurring on the extremities flexural areas and trunk. Concurrent erythrokeratoderma variabilis-like scaly plaques are commonly found in other parts of the body.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Erythrokeratoderma ”en cocardes”?
Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.
Advocacy Organizations
Syndromes Without A Name (SWAN) Australia
Provide information, support and advocacy to families caring for a child with an undiagnosed or rare genetic condition.
Clinical Trials
For a list of clinical trials in this disease area, please click here.