External auditory canal aplasia/hypoplasia

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External auditory canal aplasia/hypoplasia

Synonyms: External auditory canal stenosis/atresia

A rare otorhinolaryngological malformation characterized by failure in development of the external ear canal resulting in variable degree of malformations ranging from complete absence to mild stenosis and malformation of the middle ear. It is typically unilateral it manifests with hearing loss on the affected side and might be associated with microtia or hypoplastic pinna an aberrant facial nerve course and cholesteatoma.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024

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External auditory canal aplasia/hypoplasia?

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