External auditory canal aplasia/hypoplasia
Synonyms: External auditory canal stenosis/atresia
A rare otorhinolaryngological malformation characterized by failure in development of the external ear canal resulting in variable degree of malformations ranging from complete absence to mild stenosis and malformation of the middle ear. It is typically unilateral it manifests with hearing loss on the affected side and might be associated with microtia or hypoplastic pinna an aberrant facial nerve course and cholesteatoma.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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External auditory canal aplasia/hypoplasia?
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