Synonyms: Soft tissue perineurioma
Extraneural perineurioma is a rare tumor of cranial and spinal nerves arising from peripheral nerve sheet and composed exclusively or predominantly of cells showing perineurial differentiation. It presents as a well-circumscribed rarely encapsulated mass not associated with a recognizable nerve most commonly arising in the dermis and subcutis of the extremities or trunk or rarely in deep soft tissue or skin (e.g. in the stomach kidney pancreas maxillary sinus mandible bronchial tree and the face). The clinical presentation depends on the localization.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version February 2024
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