Familial idiopathic dilatation of the right atrium
A rare congenital heart malformation of unknown etiology that is characterized by an extremely dilated right atrium and that is usually asymptomatic and fortuitously discovered by echocardiography or chest radiography and can be sometimes associated with other anomalies such as atrial arrhythmias (e.g. atrial flutter atrial fibrillation supraventricular tachycardia) severe tricuspid regurgitation or atrial thrombus that could lead to potentially life-threatening thromboembolic complications.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Familial idiopathic dilatation of the right atrium?
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