Follicular dendritic cell sarcoma

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A rare dendritic cell neoplasm characterized by a proliferation of spindled to ovoid cells with morphological and immunophenotypic features of follicular dendritic cells. Conventional follicular dendritic cell sarcomas are negative for EBV. The tumor arises as a painless slow-growing mass in lymph nodes (most often cervical) extranodal sites (such as tonsils gastrointestinal tract soft tissue mediastinum or lung among others) or both. Paraneoplastic pemphigus may occur in rare cases. Predictive factors are tumor size presence of coagulative necrosis mitotic count and presence of significant cytological atypia.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Follicular dendritic cell sarcoma?

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My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


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