High-grade neuroendocrine carcinoma of the corpus uteri

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High-grade neuroendocrine carcinoma of the corpus uteri

Synonyms: High-grade neuroendocrine carcinoma of the uterine corpus | Poorly differentiated neuroendocrine carcinoma of the corpus uteri | Poorly differentiated neuroendocrine carcinoma of the endometrium

High-grade neuroendocrine carcinoma of the corpus uteri is an extremely rare aggressive primary uterine neoplasm originating from neuroendocrine cells scattered within the endometrium characterized macroscopically by a bulky frequently polypoid mass with abundant necrosis located in the uterus and histologically by rosette-like and cord-like structures consisting of small rounded cells with oval nuclei and scarce cytoplasm. Patients often present with dysfunctional uterine bleeding pelvic or abdominal mass and especially in later stages of the disease abdominal pain. Symptomatic metastatic spread or symptoms related to a paraneoplastic syndrome such as retinopathy or Cushing syndrome due to ectopic ACTH production may be associated.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024

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High-grade neuroendocrine carcinoma of the corpus uteri?

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Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.

Neuroendocrine Cancer Awareness Network Inc

The Neuroendocrine Cancer Awareness Network (NCAN) is a non-profit organization dedicated to raising awareness of Neuroendocrine Cancer, providing support for caregivers and people with NETs, and funding for NET cancer research. Since 2003, it has been our mission, or as we like to say, our passion, to educate and support the NET community as a whole. That’s our thing.

SALUS

Educate and provide resources to POC with Rare Cancers

Clinical Trials

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