Synonyms: IAD | Idiopathic adult ductopenia
A rare biliary tract disease characterized by loss of interlobular bile ducts resulting in chronic cholestasis without any known cause. Loss of less than 50% of interlobular bile ducts is associated with a mild disease course while loss of the majority of ducts results in a severe form potentially leading to cirrhosis and liver failure. Patients typically present as young or middle-aged adults with episodic jaundice pruritus and elevated liver enzymes.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version October 2024
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Idiopathic ductopenia?
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Advocacy Organizations
Global Liver Institute
To improve the lives of individuals and families impacted by liver disease through promoting innovation, encouraging collaboration, and scaling optimal approaches to help eradicate liver diseases.
Help Hope Live
Help Hope Live supports community-based fundraising for people with unmet medical expenses and related costs due to cell and organ transplants or catastrophic injuries and illnesses. These efforts play a critical role in helping clients access the care and equipment they need to heal, live, and thrive. Unlock a powerful and safe way to raise funds for medical needs with Help Hope Live. They provide one-on-one fundraising guidance, a customizable Campaign Page, bill pay support, and additional benefits based on their 501(c)(3) nonprofit status.
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Clinical Trials
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