Idiopathic optic perineuritis
Synonyms: Idiopathic OPN
A rare ophthalmic disorder characterized by idiopathic orbital inflammation in which the specific target tissue is the optic nerve sheath. Patients typically present with ocular pain pain on eye movement visual symptoms with loss of vision progressing over several weeks dyschromatopsia and variable visual field defects. Orbital signs and symptoms may be present and include ptosis ophthalmoplegia and exophthalmos. Optic disc edema is observed in most cases. The condition is usually unilateral.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Idiopathic optic perineuritis?
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