Isolated splenic vein thrombosis
A rare gastroenterologic disease characterized by isolated thrombotic obstruction of the splenic vein typically due to pancreatic disorders in particular acute or chronic pancreatitis or pancreatic neoplasms. It is the main cause of left-sided portal hypertension. Patients may be asymptomatic or present with abdominal pain gastrointestinal bleeding nausea and vomiting as well as signs of portal hypertension.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Isolated splenic vein thrombosis?
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Clinical Trials
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