Juvenile temporal arteritis
Synonyms: JTA | Non-giant cell granulomatous temporal arteritis with eosinophilia
A rare vasculitis characterized by mostly unilateral inflammation of the temporal artery affecting patients up to fifty years of age. Patients typically present with a lump in the temporal region or a prominent temporal artery and often have headaches. Males are more frequently affected than females and major systemic symptoms ocular complications and a biological inflammatory syndrome are usually absent although peripheral blood eosinophilia may be seen. Histopathological analysis shows arteritis predominantly of the intima with possible extension to the perivascular tissue. The presence of granuloma giant cells or fibrinoid necrosis is rare. Clinical relapses after one episode are uncommon.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024
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Juvenile temporal arteritis?
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