Late-onset focal dermal elastosis

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Late-onset focal dermal elastosis

Synonyms: PXE-like late-onset focal dermal elastosis | Pseudoxanthoma-like late-onset focal dermal elastosis

Late-onset focal dermal elastosis is a rare acquired dermis elastic tissue disorder characterized by a pseudoxanthoma elasticum-like papular eruption consisting of multiple slowly progressive asymptomatic 2-5 mm white to yellowish non-follicular papules (that tend to form cobblestone plaques) predominantly distributed over the neck axillae and flexural areas with no systemic involvement. Skin biopsy reveals a focal increase of normal-appearing elastic tissue in the reticular dermis with no calcium deposits.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

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Late-onset focal dermal elastosis?

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Clinical Trials

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