Lupus erythematosus tumidus
Synonyms: Intermittent cutaneous lupus
A rare form of chronic cutaneous lupus erythematosus characterized by extreme photosensitivity with intermittent formation of erythematous edematous urticarial-like smooth plaques on sun-exposed skin areas. The lesions heal without scarring. The course of the disease is benign and development of systemic lupus erythematosus is infrequent. Most patients do not have lupus-related autoantibodies. Skin biopsy shows a perivascular and periadnexal lymphocytic infiltrate and increased dermal mucin deposition without involvement of the dermoepidermal junction.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version December 2023
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Lupus erythematosus tumidus?
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The Fairy Goddess Mother Project Inc.
The Fairy Goddess Mother Project is a 501(c)(3) Non-profit Rare Disease Patient Advocacy Organization dedicated to increasing awareness of the little-known, often misdiagnosed disease Vulvar Lichen Sclerosus (VLS), providing financial assistance to afflicted women in need of treatment, and supporting patients’ efforts to participate in clinical trials.
the fairy goddess mother project inc
The Fairy Goddess Mother Project is dedicated to increasing awareness of Vulvar Lichen Sclerosus (VLS), providing financial assistance to women needing treatment, and supporting patient’s efforts to participate in clinical trials.
For a list of clinical trials in this disease area, please click here.