Malignant atrophic papulosis

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Malignant atrophic papulosis

Synonyms: Degos disease | Köhlmeier-Degos disease | Köhlmeier-Degos-Delort-Tricort syndrome | Papulosis atrophican maligna

Malignant atrophic papulosis (MAP) is a rare chronic thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version December 2023

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Malignant atrophic papulosis?

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