Synonyms: Extrinsic biliary compression syndrome
A rare biliary tract disease characterized by external compression and subsequent obstruction of an extrahepatic biliary duct by one or more gallstones in the cystic duct or the gallbladder. Patients may present with acute or chronic cholecystitis with right upper abdominal pain nausea and vomiting jaundice or cholangitis. Cholecystobiliary or -enteric fistulae can arise due to chronic inflammation and ulceration.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version December 2023
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Global Liver Institute
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