Mucinous adenocarcinoma of the appendix

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Mucinous adenocarcinoma of the appendix

Synonyms: Appendiceal mucinous adenocarcinoma

Mucinous adenocarcinoma of the appendix is a very rare slow growing well-differentiated epithelial neoplasm of the appendix characterized by abundant mucin production. Clinically it presents as acute appendicitis (with abdominal pain fever leukocytosis) or as pseudomyxoma peritonei (wide-spread presence of mucin within the peritoneal cavity) however some patients may be completely asymptomatic at the time of diagnosis. In many cases a second gastrointestinal malignancy is present.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version March 2024

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