Multiloculated renal cyst

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Multiloculated renal cyst

Synonyms: Multilocular cyst of the kidney | Multilocular renal cyst

A rare benign renal tumor characterized by a typically unilateral solitary multiloculated cystic mass consisting of small non-communicating cysts with flat cuboidal or hobnail epithelial lining separated by fibrous septa which may have an ovarian stroma-like appearance or be paucicellular. The tumor is surrounded by a thick fibrous capsule and does not contain solid areas or necrosis. Patients may be asymptomatic or present with a palpable abdominal mass and/or abdominal or flank pain. Age distribution is bimodal the typical age of onset being either below five or between 40 and 70 years of age.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version April 2024

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