Nasal dorsum fistula

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Nasal dorsum fistula

A rare otorhinolaryngological malformation characterized by the presence of a dermoid cyst located on the dorsum of the nose which presents a fistula often extending to the intracranial region. Patients present a firm slow-growing mass which contains skin and dermal elements (including hair follicles and sebaceous glands) that do not transilluminate or compress and may be associated with intermittent or chronic discharge of sebaceous material soft tissue and skeletal deformity and local infection. Meningitis convulsions and cerebral abscess may be observed if intracranial extension exists.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version April 2024

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