Papillary glioneuronal tumor

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Synonyms: PGNT | Pseudopapillary ganglioglioneurocytoma | Pseudopapillary neurocytoma with glial differentiation

A rare mixed neuronal-glial tumor characterized by a supratentorial space-occupying lesion in periventricular location often with prominent cystic change. The histological hallmark of this low-grade neoplasm is its pseudopapillary appearance with a single layer of cuboidal cells around hyalinized blood vessels associated with sheets or focal collections of neuronal cells. Clinical presentation is variable and non-specific most frequently with headache and seizures. Prognosis is favorable after complete resection.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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