A rare acquired dermis elastic tissue disorder characterized by multiple asymptomatic firm well-demarcated nonfollicular hypopigmented or skin-colored papules with a diameter of less than 1 cm distributed symmetrically over trunk and/or proximal limbs (rarely head neck shoulders armpits thighs) with no extracutaneous manifestations. Histopathology typically reveals decreased and fragmented elastic fibers thickened and/or homogenized collagen bundles and in some a mild perivascular lymphocytic infiltrate in the dermis.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
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