Paramedian nasal cleft
Synonyms: Alar cleft | Alar rim cleft | Cleft nose | Isolated cleft of the ala nasi | Isolated coloboma of the nose | Tessier number 1 cleft
Paramedian nasal cleft is a rare developmental defect during embryogenesis characterized by a unilateral or bilateral coloboma of the nose ranging in severity from a small notch resulting in minor deviation of the nasal septum to variable-sized clefts of the nasal ala which may be associated with small cysts or sinuses in the nasal midline. Defect may be isolated or may occur in association with cleft lip and/or other craniofacial anomalies (e.g. hypertelorism broadening of nasal root midline cleft). Dorsum and apex of nose are usually well preserved.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Paramedian nasal cleft?
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