Pemphigus erythematosus
Synonyms: Seborrheic pemphigus | Senear-Usher syndrome
A rare superficial pemphigus disease characterized clinically by well-demarcated localized erythematous scaly hyperkeratotic crusted plaques with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp and less frequently the extremities with a photoexposed distribution). Histologically granular deposits along the dermal-epidermal junction in addition to intercellular deposition in the upper epidermis are observed.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Pemphigus erythematosus?
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Advocacy Organizations
International Pemphigus & Pemphigoid Foundation
The mission of the International Pemphigus & Pemphigoid Foundation (IPPF) is to improve the quality of life for all people affected by pemphigus and pemphigoid through early diagnosis and support. Our vision is to find a cure for pemphigus and pemphigoid.
The Fairy Goddess Mother Project Inc.
The Fairy Goddess Mother Project is a 501(c)(3) Non-profit Rare Disease Patient Advocacy Organization dedicated to increasing awareness of the little-known, often misdiagnosed disease Vulvar Lichen Sclerosus (VLS), providing financial assistance to afflicted women in need of treatment, and supporting patients’ efforts to participate in clinical trials.
Clinical Trials
For a list of clinical trials in this disease area, please click here.